Abstract
A 36 years old female patient with renal staghorn caluculus associated with renal sarcoidosis was reported. Diagnosis for sarcoidosis was based on the findings such as epitheloid granuloma without caseous degeneration in the biopsy specimen from her right kidney, positive for Kveimm test, hypergammaglobulinemia, bilateral renal stones, granulomatous inflammation with foreign body reaction in the biopsy specimen from her operation scar, and conjunctival follicle. Our case is the first one in Japan, which was discovered by renal biopsy.