1980 Volume 22 Issue 4 Pages 377-384
A case (52yrs, female) of idiopathic tetroperitoneal fibrosis that developed rapidly progressive glomerulonephritis in the course of the disease was reported. Autopsy showed disseminated vasculitis of small arteries in various organs (esophagus, trachea, heart, liver, spleen and adrenal gland) and extracapillary proliferative-crescentic-glomerulonephritis with focal segmental necrotizing glomerulitis in addition to idiopathic retroperitoneal fibrosis. By an analysis of the clinical course, these lesions of the vessels and kidney were assumed to have been developed on the basis of hypersensitivity angiitis induced by contrast medium (Iodine). The possibility that vasculitis bore an etiologic relationship to idiopathic retroperitoneal fibrosis was discussed.