1977 Volume 68 Issue 4 Pages 398-406
Four cases of pheochromocytoma in one kindred were operated on and proved histologically. In this kindred two cases of von Hippel-Lindau disease were also noted. All four cases of those pheochromocytomas had norepinephrine secreting tumors and were not associated with thyroid carcinoma. In Japanese literature twenty-four cases of familial pheochromocytoma in nine families were reported so far, including those reported here, and high incidence of bilateral tumors is noted. Familial pheochromocytoma is inherited as autosomal dominant trait and probably has neuroectodermal dysplasia as a base.
