Abstract
A 44-year-old man presented with left flank pain and macrohematuria. The roentgenographic examination disclosed left hydronephrosis and stenosis of the left distal ureter. The patient was operated with the diagnosis of ureteral stricture. The frozen section during the operation revealed no malignancy. Therefore, autotransplantation of the left kidney was performed. Congo red staining revealed amyloid deposition in the resected segment of the ureter. No evidence of amyloidosis was obtained in rectal and renal biopsy. The other laboratory tests for amyloidosis were negative.
Consequently, primary localized amyloidosis of the ureter was confirmed.
Amyloidosis of the ureter is a rare entity. Review of the literature disclosed that this was the 32nd case in the world.
Clinical features of localized amyloidosis of the ureter are similar to those of ureteral tumor. Since preoperative diagnosis is difficult, nephroureterectomy is usually performed for this disease. There were only two cases prior to ours which were treated by autotransplantation of the kidney.
In the discussion, localized amyloidosis of the ureter was statistically analysed by reviewing the literature. The indication and advantages of autotransplantation of the kidney were also described.
