1998 Volume 31 Issue 10 Pages 1347-1350
A 40-year-old woman with multiple renal cysts in addition to bilateral renal angiomyolipomas (AML) and tuberous sclerosis who required hemodialysis treatment for chronic renal failure was reported. In spite of the high incidence of the renal involvement in patient with tuberous sclerosis, the occurrence of chronic renal failure is rare. Renal AML alone may have less potential for producing severe renal failure because of its limited growth potential, while renal cysts may enlarge and cause renal impairment by replacing and compressing normal tissues. In light of the concomitant presence of multiple renal cysts, it is extremely rare that end-staged renal failure is the result of bilateral AML. In addition, it is emphasized that careful management is required to prevent intratumoral bleeding from AML when conservative manegement is selected.