Abstract

  A 32-year-old man was pointed out a complete situs inversus when he was a child. He had an operation for single right ventricle at the age of 22. He took postoperative follow-up at the department of pediatric cardiology, and a blood test revealed liver dysfunction. Contrast-enhanced CT imaging found out an enhanced lobulated mass of 10mm in the right side of the aorta. Therefore he consulted the department of endocrinology. The value of noradrenaline was above limit in his blood and urine, and MIBG scintigraphy identified a tumor, which was pointed out in the former CT scan. The diagnosis was paraganglioma. He received a retroperitoneoscopic resection of the tumor. During the operation, his systolic blood pressure temporarily elevated to 180 mmHg, but his vital signs ware stable in general. The specimen was reddish brown and the margin between the tumor and the normal tissue was clear macroscopically. The pathological finding was nesting or trabecular pattern of cells with abundant granuler eosinophilic or basophilic cytoplasm. There ware no perioperative adverse events. He is now followed up at our hospital.

  Paraganglioma with a complete situs inversus is very rare, and this is the first report in our country in which the resection was performed laparoscopically.