Case of Arnold-Chiari malformation

Abstract

A 31-year-old female complained of headache and giddiness followed later by unsteady gait. These symptoms were not definitely diagnosed with the conventional X-ray examination, however, ENG test revealed down-beat nystagmus during positioning test, impaired fixation-suppression of caloric nystagmus, and inverted optokinetic responses. From these findings described above, the central nervous system disorders, such as brainstem and/or cerebellar lesions were strongly suggested. A definite diagnosis was established with the neuroradiological examinations.
Hence, neurotological examinations are considered to be one of the most reliable functional measures in the diagnosis of brainstem lensions.