Successful treatment with hysteroscopic surgery for OHVIRA syndrome that was diagnosed before the surgery

Abstract

  OHVIRA (Obstructed Hemivagina and Ipsilateral Renal Anomaly) syndrome is characterized by double uterus, double vagina, one-sided vaginal obstruction that causes hemivaginal hematoma, and congenital renal defects on the same side as the hematoma. A woman generally develops this syndrome during her puberty, possibly before her first experience of sexual intercourse. The presence of these conditions often makes both, pelvic examination and transvaginal ultrasonography challenging for establishing a preoperative diagnosis of OHVIRA syndrome. Our 13-year-old patient underwent the following diagnostic procedures before the surgery: transvaginal ultrasonographic scanning, pelvic magnetic resonance imaging, and abdominal computed tomography; thereafter, transvaginal resectoscopic surgery for the obstructed vagina was performed successfully. A resectoscope gave a good transvaginal view in the small hemivaginal vault of each side.