Abstract
We present a rare case of an infant with life-threatening congenital tracheal stenosis with esophageal atresia and coarctation of the aorta. Airway management was very difficult due to large-bore and long residual esophageal fistula and extensive, severe tracheal stenosis. Furthermore, recurrent episode of tracheal granulation and pulmonary atelectasis exacerbated pulmonary gas exchange. Aggressive use of bronchofiber scope was considered to be essential for the diagnosis of ventilatory failure. The patient received tracheoplasty at 6 months, and is still been managed under mechanical ventilation.