Abstract
A 29-year-old man was diagnosed with pulmonary arterial hypertension (PAH) 5 years ago. He had not been treated for PAH. He was transferred to our hospital after visiting a nearby hospital for chest pain and being diagnosed with pulmonary artery dissection. After admission, he emergently underwent a prosthetic graft replacement of the main pulmonary artery and bilateral pulmonary artery plication. Subsequently, he was transferred to the ICU and we immediately started aggressive treatment for the refractory PAH including multiple medications therapy, strict sedation and mechanical ventilation. Good control of PAH was achieved, and he was finally extubated on POD 21, discharged from the ICU on POD 29, and discharged from the hospital on POD 101. Because the mortality rate of PAD is very high, early surgery and strict postoperative management are required.
