Journal of The Showa Medical Association
Online ISSN : 2185-0976
Print ISSN : 0037-4342
ISSN-L : 0037-4342
Case Report
A CASE OF MCCUNE-ALBRIGHT SYNDROME WITH FEMORAL TROCHANTERIC FRACTURE AND ADVANCED COXA VARA
Satoshi KATAGIRIHisahiro KUMAMOTOFumio SUKEZAKIMasanori NAKAMURAHideyo MIYAOKA
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2009 Volume 69 Issue 2 Pages 194-197

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Abstract
McCune-Albright syndrome is associated with recurrent fractures due to fragile bones from fibrous dysplasia, causing deformed coxa vara (also called Shepherd's crook deformity) in the femur. We report a case of coxa vara after a fracture due to a fall in a child with McCune-Albright syndrome. The patient was a six-year-old female diagnosed with McCune-Albright syndrome. She received conservative therapy with traction treatment for the femoral trochanteric fracture due to a fall. She repeated synostoses and fractures during the course of the treatment. The fractures were completely united after about 8 months of treatment. However, the deformed coxa vara of the hip joint subsequently worsened without pain and in the unaffected side. We prefer conservative therapy taking into consideration the patients age, but surgical procedures are usually considered when bones are mature. Nevertheless, some repots suggest that this kind of case is often difficult to treat, even if surgical procedures are done. There are few reports on patients with McCune-Albright syndrome, and further reports are required.
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© 2009 The Showa University Society
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