Abstract
Childhood Sjögren’s Disease (CSD) often presents with a variety of extraglandular symptoms, including fever, fatigue, arthralgia, and lymph node swelling, making diagnosis difficult without proactive suspicion. We report a case in which CSD was diagnosed based ranula and parotid gland swelling. The patient was a 16-year-old girl. For the past year, she had experienced intermittent parotid gland swelling only during meals. Six months prior, she had also developed oral floor swelling and visited our department. Blood tests showed positive results for anti-SS-A/Ro antibodies and anti-SS-B/La antibodies, and elevated IgG levels. Although she did not report experiencing dry mouth, a Saxon test showed decreased secretion, and a lip biopsy revealed lymphocyte infiltration, leading to a diagnosis of CSD. The parotid gland swelling disappeared with pilocarpine hydrochloride administration, and there has been no recurrence. No other collagen diseases were found, and the patient is currently under observation in internal medicine. Since CSD is a chronic disease, it may not be detectable at the time of testing, and repeated testing is necessary for suspected cases.