Abstract
Infantile f ibrosarcoma is very rare, comprising only 0.4% of all infant tumors, and it most often develops in the soft tissue of a limb. Reported oral cases of this tumor include 3 cases occurring in soft tissue and 1 case occurring in mandibular bone. Infantile f ibrosarcoma develops more rapidly than adult form, with faster tumor growth. Its metastatic rate is 7.3% to 8.3%, although there is a high degree of resorption of bony tissue (which is normally associated with aggressively metastatic tumors) . Surgery is considered the best treatment option, because local recurrence after extensive resection is qutie rare. The five-year survival rate of this tumor is 50% to 85%, although is differs with age at onset. A nine year-old girl with intaosseous maxillary tumor was treated with Interleukin-2 (Imunace®, Shionogi, Osaka, Japan ; 7×105 JRU/day), and underwent radical resection of the maxilla ( both sides of which contained impacted canines) under general anesthesia. After wound healing, her occlusal disturbance and facial def omity were improved by maxillf acial prosthesis. Five years after treatment, her progress was good, without recurrence or metastasis.
