Abstract
We report here a rare case of 13-years old boy with allergic granulomatous angiitis (AGA, Churg-Strauss Syndrome). He had chest pain, arthralgia at the shoulders, numbness of hand fingers, skin rash, loss of body weight, subcutaneous nodosa, and abdominal pain. Laboratory investigations demonstrated peripheral blood eosinophilia, increase of ESR, hypergamma-globulinemia, positive CRP test, and liver dysfunction. Immunologic examinations revealed positive rheumatoid factor. UCG revealed partial hypokinesis of left ventricle, Typical pathological findings were obtained from skin biopsy. He died about 3 months after the onset of vasculitic illness. The cause of death was thought to be cardiac failure induced by widespread myocardial necrosis.
Great caution should be exerted in cardiac involvement of AGA.
