Abstract
Oral-facial-digital syndrome (OFD syndrome) is a hereditary syndrome. The main signs are oral cavity abnormality (ligule, a fraenum in the oral cavity, and tooth socket irregularity), and perodactylia (brachydactyly, syndactylism, and many fingers).This is a case report of a female of biovular twins, 4 years and 5 months old at the time diagnosis with OFD syndrome that was brought to our hospital to have her oral cavity cleaned and receive guidance on chewing and deglutition. X-rays were taken of her body from head to foot. Abnormality of the lips and cheeks fraenum and hypoplasia of the teeth was seen in the x-ray images. Also, the oral cavity views showed a native lack of the side incisive tooth.Patients of OFD syndrome have oral cavity abnormalities, so it is necessary for them to take close care of their dental health over the long term. Otherwise there is the possibility of problems in articulation functions, feeding functions, and/or deglutition.