2009 Volume 47 Issue 5 Pages 767-772
Dystrophic epidermolysis bullosa (DEB) is a group of rare genetic skin disorders with bullae caused by mechanical stimulus. The dental health care of small children with dystrophic type of EB was described in this paper.A 3-year-old girl with DEB visited the Okayama University Pediatric Dental clinic with a letter of referral from the pediatrician. The patient had severe caries and experienced a high level of dental fear. Thus, dental examination and treatment posted a big problem. We planned (1) Improvement of management (2) Improvement of oral hygiene (3) Arrest of present caries, and scheduled for her recall once every two weeks.The Tell-Show-Do technique was performed to build up trust and confidence with the child. The toothbrush was also re-designed to provide maximum care in decreasing plaque. Fluoride application in the clinic was done. The patient was provided with a mouth wash containing fluoride for homeuse. A normal eruption of permanent teeth were observed from then on. Eventually, the patient's appetite improved.Patient with DEB should be managed by first building up mutual trust and confidence to pare the way for ease in oral health care.
