A Case Report of Marshall Syndrome

Abstract

Marshall Syndrome was first reported in 1958 by Marshall in a kindred of seven individuals over three generations. The distinctive symptoms of this rare syndrome are hearing impairment, myopia,cataracts, and retracted midface. We provided dental care to a 4-year-old patient with Marshall Syndrome. The facial characteristics of this patient included retracted midface, shallow orbit and upward naris. The maxillary dental arch had a trapezoidal form. The maxillary arch width was greater, the arch length smaller and all deciduous mesiodistal crown diameters were larger than the mean values reported by the Japanese Society of Pediatric Dentistry (1995). The eruption space for the maxillary permanent incisor teeth was estimated to be insufficient by X-ray photograph. As there are few reports of Marshall Syndrome, it is difficult to determine the constitutional growth. The patient is under periodic dental observation.