Abstract
Hereditary opalescent dentin is a localized dysplasia affecting the dentin, and also called Dentinogenesis imperfecta.
The patient (a three-year three-months-oldboy) diagnosed as having Hereditary opalescent dentin with no Osteogenesis imperfecta, visited the Pedodontics Clinic of Osaka University Dental School.
The findings were as follows:
1) Erupted teeth ?? ?? ?? showed a peculiar opalescent color and severe attrition.
2) Typical reduction in the size of pulp cavities was observed on the deciduous molars.
3) Histrogical observations showed cementum of normal structure, but enamel prisms and dentinal tubules were greatly reduced in number, and they appeared to be irregular.
4) This trait was observed to be autosomal dominant with high penetrance. In order to regain the vertical dimension, an over-denture was placed on the teeth, after stainless steel crowns were placed on the deciduous molars.
