Abstract
A case of a linear nevus sebaceous syndrome in an 8-year-old girl was investigated.
The patient was the product of a 37-week gestation and normel vaginal delivery from an 27-year-old mother and a 27-year-old father. The family history was negative with respect to any congenital deformity. At birth, linear nevus sebaceous extended from the froehead to the upper lip. She also manifested convulsions and mental retardation.
Oral examination showed the following:
1. The oral lesions were limited to the right side, agreeing with the predominant side of the linear nevus on the face, the abnormalities of electroencephalogram, and the enlargement of the lateral ventricle in the pneumoencephalogeaphy.
2. The carpal bones radiograph demonstrated normal development of bone, and skull radiographs showed no morphological abnormalities of the skull and face. The cephalogram illustrated the enlargement of mandibular angle and upper and lower alveolar protrusion.
3. The number of permanent teeth was normal, but the upper right central and lateral incisors nad the canine showed morphological abnormalities and ectopic eruption. The mesio-distal lengths of 64321 were from 4 SD to 6 SD, larger than the Japanese mean Values.
4. Oral mucosal involvement was limited to the right side, as mentioned above. The upper lip, cheek, and tongue appeared whitish and lacking in tension. The gingiva showde inflammatious hypertrophy. The palatine mucosa appeared to be of normal color, but showed surface roughness and lacked transverse palatine ridges. There was swelling in the right side palate. It was rather fluidi.
5. Biopsy of a gingival lesion showed parakeratosis and a palatal lesion showed parakeratosis and elongation of the rete ridge.
