Abstract
In 1954 Bloom first described the Bloom syndrome, which was characterized by congenital telangiectatic erythema, sun sensitivity of the skin and low-birthweight dwarfism, about 100 cases of this syndrome have been reported on throughout the world and about 6 cases in Japan. However few oral minifestations have been described in the reports.
Two sublings with the Bloom syndrome, a 12-year-old boy and a 10 yearold girl requiring dental care, had been refered to the Pedodontics, Asahi Univ. Hospital.
The following are the dental findings.
1) General findings:
The two sibling patients were bone from the parents of a consanguineous marriage. Three typical symptoms associated with this syndrome, as described above, were seen in both patients. Marked retardation in physical growth both height and weight of the body were noticed, this being more prominent in the elder brother.
2) Oral findings:
Congenital missing of the lower bilateral canines in the elder brother was observed and generally smaller tooth size was characteristic. Also either the length and the width of dental arch, and basal arch were measured to be smaller when compared with the normal, while in the younger sister, the tooth material was shown to be within normal 1 S. D. values except for lower first molers.
3) Cephalometric findings:
Retardation of the growth of the gnatho-facial bone was recognized in both cases as well as seen in the physical growth. Particularly marked retardation was observed in the mandibularbone. Affects of the Bloom syndrome on the maxillo-facial and oral cavity were considered to be more evident in the elder brother than in the younger sister.
