The Japanese Journal of Pediatric Dentistry
Online ISSN : 2186-5078
Print ISSN : 0583-1199
ISSN-L : 0583-1199
A Case Report on the Silver-Russell Syndrome and Its Dental Findings
Masumi FujiiEriko YanagidaKinjiro SatYoshiyuki FunakoshiToyoji Hieda
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JOURNAL FREE ACCESS

1988 Volume 26 Issue 1 Pages 186-195

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Abstract
The Silver-Russell syndrome is a type of intrauterine growth retardation, characterized by low birth weight at term, shortness of stature, asymmetry of body, variation in sexual development, pseudohydrocephalus, triangular shape of face and inverted V shape of mouth, and so on.
This syndrome is described in a 4-year,1-month-old girl, who had a low birth weitht at term, shortness of stature, asymmetry of body, pseudohydrocephalus, triangular shape of face, in-curved fifth fingers, micrognathia and low set ears. In addition to these general findings, this case also disclosed the following dental findings:
1) Each of the mesiodistal lengths of all primary teeth were smaller than the standard size.
2) The form of the mandibular dental arch was asymmetrical.
3) Roentgenogram revealed large pulp chambers in the primary teeth, especially in primary canines and primary molars.
4) The mandibular body and ramus showed insufficient growth, according to cephalogram analysis.
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© The Japanese Society of Pediatric Dentistry
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