Abstract
Cleidocranial dysplasia is a form of congenital systemic bone dysplasia, that has such clinical characteristics as aplastic or hypoplastic clavicles bilaterally, delayed ossification of the skull, as well as delayed deciduous dentition and jaw bone development. In Japan, many cases have been reported. We experienced a case of cleidocranial dysplasia in a 6-year,10-month old girl.
This case showed hypoplastic development of the skull, and defect of the clavicles. This patient had prolonged retention of the deciduous teeth and delayed eruption of the permanent teeth. The orthopantomography findings showed no root resorptions of the deciduous teeth. Development age of the permanent teeth was delayed about two years. The size, number and form of the teeth were usual. The width and length of both the maxilla and mandible dental arches were underdeveloped. According to X-ray cephalometric analysis, the labial tapping of the maxilla anterior and lingual tapping of mandible anterior was shown.
