Abstract
Rieger's Syndrome is an autosomal-dominant heritable disorder with triad of hypoplasia of the anterior iris stroma, bridging angle of the iris strands and posterior embryotoxon. Other various clinical findings were manifested due to abnormal development of the mesodermal tissue. The present findings of a sixyearold boy affected with Rieger's Syndrome were as follows.
1. Three irregular pupilla, cloudy cornea and auricular septal defects.
2. Low body height and delay of bone age.
3. Microdontia of the lateral upper incisors and delay of calcification of the upper second premolars
.4. Hypoplasia of the maxilla and anterior crossbite.
5. Occlusal correction of the anterior crossbite using a Frankel type III unit.
