Abstract
Oculo-dento-digital syndrome is an autosomal dominant disorder with a small orbita, hypoplasia of the nasal wing and digital anomaly of the hands and feet due to ectodermal dysplasia. It is one of the most interesting congenital diseases in dentistry because of various clinical manifestations of hypoplasia of the tooth and jaw. The present findings of a four-year-old girl affected with Oculo-dento-digital syndrome were as follows.
1. Rough and short hair.
2. Microphthalmus, ocular hypotelorism and repaired bilateral fusion of the eye lids.
3. Repaired bilateral syndactyly of the forth and fifth fingers in the hand.
4. Morphological anomaly of the condyle and cronoid process.
5. Hypoplasia of the teeth and narrowed pulpal cavity.
6. Abnormal horizontal absorption of the alveolar bone.7. Congenital missing of the right second premolars.
