Abstract
The Ellis-van Creveld syndrome is a rare herediatry disorder accompanied by chondrodysplasia, polydactly of the hand, ectodermal dysplasia, and congenital heart malformations. A 6-year-5 month old male was first examined at the Pedodontic Clinic of Kobe Children's Hospital because o-f aesthetic problems.
The skeltal anomalies, ectodermal dysplasia, polydactly of the hands and congenital heart disease were observed. The dental anomalies were congenital missing teeth, malformed teeth, occulusal anomalies, an oral vestibulum anomaly, and a superior-inferiorlabial frenumanomaly. The mesio-distal width of the deciduous teeth and the width of the dental arch were smaller than the standard average. Analysis using cephalometric radiography revealed a relatively flattened genial angle. Upper and lower anterior acrylic partial dentures were constructed to maintain space, and to improve mastication.
