Abstract
Peutz-Jeghers syndrom is an autosomal dominant inheritance disease characterized by polyposis of the gut and pigmentation of the lips and oral mucosa.
A 4-years-1O-months-old boy having an intraoral pigmentation had visited the Clinic of Pedodontics, Kobe Children's Hospital. And he was refered to the surgery with the suspect of Peutz-Jeghers syndrom, and has been checked periodically there for polyps. When he was 9-years-8-months,11years, and 11-years-7-months-old, polyps were found in his stomach, sigmond colon and/or recutum, and they were all removed by endscopic recection, After that he progressed favorably without recurence of any polyps. In the dental Clinic, therefore, any patient found to have an intraoral pigmentation should be refered to the, surgery with the suspition of the Peutz-Jeghers syndrom.
