2016 Volume 53 Issue 3 Pages 294-299
Dermatofibrosarcoma protuberans (DFSP) is a rare disease in infants and is classified as an intermediate-grade malignancy. The characteristics of the tumor are limited metastasis, slow local but aggressive growth, tendency to recur locally, and rarely a depressed lesion. We report on the case of a 12-year-old boy who developed DFSP on his left chest at five years of age. The patient was suspected to have angioma or lymphangioma and has been followed up at the outpatient clinic in our hospital. Over a period of seven years, the tumor increased in size and showed both protuberant lesions and depressed lesions. We suspected malignant soft tissue tumor, such as sarcoma, on the basis of ultrasonography and magnetic resonance imaging (MRI) findings. The tumor was excised, and its histopathological analysis indicated benign tumor with spindle cells. However, the permanent specimen demonstrated DFSP. We then excised the residual tumor including a wider margin. We found a rare type of DFSP with a depressed epidermis. The boy was surgically treated. DFSP did not recur nor metastasize in the two years of follow up.
