The Japanese Journal of Pediatric Hematology / Oncology
Online ISSN : 2189-5384
Print ISSN : 2187-011X
ISSN-L : 2187-011X
Case Report
A case of primary inflammatory myofibroblastic tumor of the jejunum presenting with hemorrhage and severe anemia
Ririko TakemuraYuki NoguchiDaichi SakaiMasayuki YoshidaRei MatsuuraSatoshi UmedaMasahiro ZenitaniNoriaki UsuiMakoto Takeuchi
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2025 Volume 62 Issue 1 Pages 59-62

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Abstract

An 11-year-old girl with worsening shortness of breath and a pale complexion presented with anemia (hemoglobin; 6.8 g/dL). Abdominal computed tomography revealed a small intestinal mass. The small intestine was resected partially. Intraoperative findings revealed a mass protruding from the intestinal wall, primarily in the jejunal submucosa. Histopathological examination revealed an inflammatory myo­fibroblastic tumor (IMT), which is an intermediately malignant tumor that can occur anywhere in the body. Pathological immunohistochemical staining, especially for ALK positivity, is useful for diagnosis. Complete resection is crucial for successful treatment of IMT, and prognosis after resection is good. As local recurrence and metastasis have been reported, long-term follow-up using imaging is required. Ten months after resection without adjuvant therapy, the patient was well and did not experience any recurrence.

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© 2025 The Japanese Society of Pediatric Hematology / Oncology
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