2025 Volume 62 Issue 1 Pages 59-62
An 11-year-old girl with worsening shortness of breath and a pale complexion presented with anemia (hemoglobin; 6.8 g/dL). Abdominal computed tomography revealed a small intestinal mass. The small intestine was resected partially. Intraoperative findings revealed a mass protruding from the intestinal wall, primarily in the jejunal submucosa. Histopathological examination revealed an inflammatory myofibroblastic tumor (IMT), which is an intermediately malignant tumor that can occur anywhere in the body. Pathological immunohistochemical staining, especially for ALK positivity, is useful for diagnosis. Complete resection is crucial for successful treatment of IMT, and prognosis after resection is good. As local recurrence and metastasis have been reported, long-term follow-up using imaging is required. Ten months after resection without adjuvant therapy, the patient was well and did not experience any recurrence.