Abstract
Recently, several reports suggest the abnormalities of cerebral venous system in Struge-Weber syndrome. We present a case of Sturge-Weber syndrome in a 13 year old female with convulsion, right hemiparesis and motor aphasia, in association with rectal sinus thrombosis. In the acute stage, carotid angiography revealed cerebral venous anomalies and disappearance of rectal sinus. Enhanced CT represented particular gyral enhancement on damaged hemisphere. Two weeks after the onset, the second carotid angiography indicated the recanalization of rectal sinus and gyral enhancement on repeat CT was diminished. The clinical course was septic. She was treated by antibiotics, anticonvulsants and antiplatelet agents. The inflammation of otolaryngeal lesion was supposed to be the cause of sinus thrombosis. After the recanalization of rectal sinus, she was rapidly improved.
