Abstract
Microscopic polyangiitis (MPA) is characterized by the inflammation of small-sized vessels. We herein describe a patient with MPA who had suffered repeated large vessel diseases. A 63-year-old woman who had been given a diagnosis of MPA suffered Stanford type B aortic dissection 3 times in 3 months. Computed tomography (CT) after six months revealed that the descending aorta was dilated to 60 mm, and we performed descending aortic replacement. One year after the first operation, because CT showed a saccular aneurysm of aortic arch, we performed total arch replacement, without any complications.