Abstract
A 30-year-old woman of 30 weeks gestation was transferred to our hospital due to sudden onset backpain and dyspnea. Enhanced computed tomography and echocardiography revealed Stanford type A acute aortic dissection with aortic regurgitation. Marfan syndrome was suspected in this patient because her mother had died of aortic dissection following a diagnosis of Marfan syndrome before. Immediate operation of aortic repair was required. However, due to the risk of massive bleeding from her uterus and placental separation site due to cardiopulmonary bypass with heparin administration, emergency caesarian section was initially performed. Twelve hours later, graft replacement of the ascending aorta was performed secondarily. The postoperative courses of the mother and infant were uneventful.
