Abstract
A 32-years-old man had undergone ventricular septal defect patch closure and patent ductus arteriosus ligation for a ventricular septal defect, patent ductus arteriosus, coarctation of the aorta, and pulmonary hypertension at the age of one year. He was then followed up for aortic coarctation under a presumed diagnosis of pseudocoarctation of the aorta because the pressure gradient was mild (≤10 mmHg) postoperatively. Furthermore, he had required aortic valve commissurotomy for aortic stenosis due to a bicuspid aortic valve at 17-years of age. Subsequently, aortic stenosis and insufficiency had gradually worsened and a chest computerized tomography scan revealed an ascending aortic aneurysm. We performed the modified Bentall procedure using a mechanical heart valve and a Dacron graft, and total arch replacement including resection of the aortic coarctation using a 4-branched Dacron graft. Surgical treatment for the aortic aneurysm with pseudocoarctation is rare, and the surgical approach varies according to the position of the aortic aneurysm. We examined the surgical strategy for aortic aneurysm treatment with pseudocoarctation by referring to reported cases.