Aortic Dissection with Polycystic Kidney Disease and Cystic Necrosis within Arterial Media

Abstract

We report a 34-year-old man, who was diagnosed Stanford type A acute aortic dissection with polycystic kidney disease (PKD) and had received Bentall’s Operation (using SJM 25 mm and Carboseal 28 mm). The postoperative course was good and he left the hospital without renal dysfunction. Pathological finding revealed cystic medial necrosis at aorta. PKD caused cysts to grow inside the kidneys and the complications of PKD are cerebral aneurysm and acute aortic dissection, which could develop sudden death. It is considered, appropriate preventive methods and treatment strategies are required considering acute aortic dissection as a complication of PKD.