2022 Volume 31 Issue 1 Pages 11-14
A combination of Moyamoya disease and abdominal aortic aneurysm is extremely rare. Moyamoya disease carries the risk of perioperative brain hemorrhage or infarction. We report a successful endovascular aneurysm repair for abdominal aortic aneurysm in Moyamoya disease while monitoring parameters including blood pressure, partial pressure of carbon dioxide in arterial blood, and regional cerebral oxygen saturation. No neurological abnormalities observed in the perioperative period. Endovascular aneurysm repair entails less risk of hemodynamic instability than open repair, and could therefore be an option for abdominal aortic aneurysm repair in Moyamoya disease.