2024 Volume 33 Issue 4 Pages 223-227
In rare cases, neurofibromatosis type 1 (NF1) follows a fatal course due to spontaneous artery ruptures because of vascular fragility. We report a case of successful stent graft treatment for spontaneous rupture of the subclavian artery, in a patient with NF1. A 72-year-old woman with a history of NF1 suddenly lost consciousness seven days after surgery for a strangulated ileus. She suffered a massive hemothorax due to spontaneous rupture of the left subclavian artery, leading to cardiac arrest. After resuscitation, emergency evasive stent graft treatment for hemostasis was successfully performed in 8 min, through a left brachial percutaneous approach, by introducing and deploying a Viabahn VBX stent graft into the left subclavian artery from just below the vertebral artery bifurcation. On the 43rd postoperative day, she was transferred, with a walker, to a rehabilitation hospital. We have successfully performed a stent graft treatment for rapid hemostasis with a minimally invasive technique, even in this case of spontaneous artery rupture of NF1. However, since it is difficult to accurately detect fragile vessels in NF1, the safety of stent graft treatment requires further case studies.
