Abstract
A 63-year-old female patient with Cruveilhier-Baumgarten disease is reported.
She had an episode of hematemesis due to a rupture of the esophageal varices. She showed splenomegaly with hypersplenism, dilatation of the abdominal vein, and venous hum in the right upper quadrant. A Celiac angiography demonstrated a marked dilatation of the umbilical vein and the portal vein, and splenomegaly. On laparoscopy, the liver was atrophic and its surface was smooth. A histological finding of the biopsied liver showed that there was mild fibrosis with minimal infiltration of the lylnphocyte in the portal area. There was no evidence of liver cirrhosis. A dilated umbilical vein seemed to be congenital. The definition of Creveilhier-Baumgarten disease and tis etiology were discussed.
