A case report of primary extranodal non-Hodgkin's lymphoma of the extrahepatic bile duct

Abstract

A 60-year-old man complaining of sudden epigastralgia followed by jaundice was admitted to Osaka Kousei-nenkin Hospital. A percutaneous transhepatic cholangiogram showed long tapered stricture of the extrahepatic bile duct. An abdominal angiography revealed severe stenosis of the portal vein at the porta hepatis. We diagnosed a cholangiocarcinoma and performed biliry decompression by internal drainage and chemotherapy. One year later, as the patient was in fair condition whose biliary stenotic lesion was not developed and stenosis of the portal vein was disappeared, the patient underwent a laparotomy. Pathological examination showed a diffuse non-Hodgkin's lymphoma, medium sized cell type arising from extrahepatic bile duct. Primary m alignant lymphoma of extrahepatic bile duct is very rate; there is a report of well-documented case by Nguyen and this case is the first report in Japan.