Abstract
Extracardiac rhabdomyoma is rare benign tumor found in soft tissue. The majority of instances of extracardiac rhabdomyoma arise in the head and neck regions. Rhabdomyomas are classified into adult and fetal variants. A case of adult rhabdomyoma occurring in the larynx, which appeared in a 29-year-old lady, was reported. The tumor was removed surgically by the laryngofissure approach. The patient remains free of disease at the present time. The clinicopathological features of the tumor are presented with a review the pertinent literature.