Abstract
A 45-year-old woman who had been treated for five years under the diagnosis of aortitis syndrome, had fever and raised, red, tender nodules and plaques on the right cheek. Neutrophilia, elevated ESR, and positive CRP were evident. The histological findings of the red nodules were compatible with the diagnosis of Sweet’s syndrome. The eruption cleared without scarring with daily oral administration of 50 mg prednisolone, but acne-like eruptions appeared on the face when the dose of prodenisolone was reduced. The eruption finally faded with daily oral aciministration of 7.5mg prednisolone for about one and a half years after it first appeared. This case is the first report of Sweet’s syndrome associatied with aortitis syndrome and we discussed the relationship between Sweet’s syndrome and pyoderma gangrenosum.