Abstract
A case of “so-called” sclerodermatomyositis is reported. A 56-year-old man with extensive diffuse skin sclerosis complained of muscle weakness and pain. Physical examination revealed marked erythematous changes as well as diffuse skin sclerosis and pigmentation. Laboratory examination showed positive antinuclear antibodies (speckled pattern) and elevated myogenic enzyme activities in the serum. Esophageal dysfunction and lung fibrosis were also present. Histopathological examinations of the skin and muscle were consistent with scleroderma and myositis, respectively, the latter being confirmed by electromyography as well. Immunohistochemical staining revealed that most of the infiltrating cells were activated T lymphocytes.
