Abstract
A case of nerve sheath myxoma on the right buttock of a 16-year-old female is reported. The tumor was skin-colored and elastic hard in consistency. A similar nodule was palpable in the dermis. No café-au-lait spot was observed anywhere on the body. A lobulation was noticed on the cut surface of the resected mass, and light microscopy revealed mucinous lobules gathered in the dermis. Spindle-shaped cells were noticed in each lobule and showed little pleomorphism, thus leading to the diagnosis of nerve sheath myxoma. Immunohistochemically, S-100 protein was weakly positive and epithelial membrane antigen was negative in the tumor cells, raising the possibility that this tumor might be derived from Schwann cells.
