Abstract
We report a 54-year-old Japanese male with pseudoxanthoma elasticum with angioid streaks (Grönblad-Strandberg syndrome). He manifested the typical features of skin changes and angioid streaks on bilateral fundoscopy. However, the patient did not have any other complications. The histopathological findings of a skin biopsy specimen obtained from the neck revealed the fragmentation and clumping of elastic fibers in the middle dermis.