2016 Volume 78 Issue 6 Pages 613-616
An 8-day-old female baby visited our clinic with erythema, bullae formation, scale, and crust on the whole body, mainly on the extremities. She was born at full term by a natural birth. Histopathological examination of the dorsum of the right great toe revealed severe hyperkeratosis and acanthosis with epidermal edema. In the upper dermis there were heavy perivascular infiltrations of lymphocytes, including eosinophils. We applied only white soft paraffin onto her whole body. The erythema gradually disappeared and linear verrucous papules appeared on the extremities after 1 month. At 5 months,reticular and spiral pigmentation on the whole body became her main complaint. In addition, she had a vasa sanguinea retinae aberration in the left eye (vascular expansion and tortuosity with aberrant anastomosis) and retinal apoplexy. The vascular expansion and tortuosity were improved by photocoagulation. We thought that this was a typical case of Bloch-Sulzberger syndrome (also known as incontinentia pigmenti), in which we observed the eruptions from the inflammatory stage to the pigment stage.
