Two Cases of Membranous Lipodystrophy (Nasu)

Abstract

Two cases of membranous lipostrophy (Nasu) were reported. The first case was a 22 Years old male, who feeled pain in the both ankles. Roentgenograms revealed multiple symmetrical radiolocent areas. He had no psychiatric disorder. His both grandfathers were cousin. Exicion of the lesion disclosed soft, yellow and fatty tissues. Characteristic membranous structures were noted in microscopic observations. The second case was a 32 years old female, who showed various types of psyatric disorders. Her parents were cousin. A psyatrist accidentally found skeletal abnormalities on X-ray. Our further radiological surveys revealed multiple symmetrical radiolucent areas. The histological findings were identical with the first case.