Abstract
A case of 3year-old boy with recurrent polyneuropathy was described. The initial attack disappeared about three months after the onset of the symptoms with corticosteroid treatment. However, he had weakness and gait disturbance two months after the discontinuation of the treat-ment.
Sural nerve biopsy performed before the readministration of corticosteroid revealed the loss of large myelinated fibers, the neuronal fibrosis, the appearance of macrophages, and the initial stage of onion-bulb formation.
Since one week after the readministration of corticosteroid, he was able to walk with support and his other neurological symtoms disappeared gradually. The corticosteroid was discontinuated five months later. Thereafter he has had no neurological symtoms till now.
