Abstract
A case of moyamoya disease, accompanied with hypertension, was presented.
The patient, 4 years of age, was attacked by sudden paresis of the extremities. CAG showed conspicuous narrowing at the beginning of the ophthalmic, anterior cerebral and posterior cerebral arteries. Unusual net-like collaterals were also noted at the base of cerebrum. Right internal carotid artery showed alternating zones of widening and narrowing of the arte rial lumen at about 3cm. above the bifurcation.
Right renal artery was composed of two branches and showed marked narrowing at the beginning.
From angiographic findings, the authors concluded that the symptomes and signs of this patient were originally caused by systemic dis ease of the arteries, “fibromuscular dysplasia”.
