Abstract
We present a case of congenital cholesteatoma associated with pars flaccida cholesteatoma. A 53-year-old man presented with a few years' history of left hearing loss. Based on the detection of attic retraction, we made the diagnosis of pars flaccida cholesteatoma. When trans-canal atticotomy was performed, a white mass appeared anterior to the tensor tympani.
Thus, the patient had congenital cholesteatoma associated with a pars flaccida cholesteatoma, that is, he had two different types of cholesteatomas.
In most cases, congenital cholesteatoma exists in the anterior or posterior quadrant of the tympanic membrane, whereas in this case, it was found in the attic. Cases with congenital cholesteatoma present only in the attic are unusual. In this case, the congenital cholesteatoma blocked attic aeration, isolating the attic.
We concluded that this may have resulted in some infection, leading to the formation of acquired pars flaccida cholesteatoma.
