Abstract
Angiomyolipoma is a benign tumor that most commonly forms in the kidney and is sometimes associated with tuberous sclerosis. Here we report a rare case of angiomyolipoma of the nasal cavity. A 56-year-old male patient presented with a firm swelling in his right nasal vestibule. A CT scan revealed a mass in the right nasal vestibule without bony destruction. The patient had no clinical signs of tuberous sclerosis. The tumor was completely extirpated via a transoral approach, and the diagnosis of angiomyolipoma was confirmed histopathologically. The patient has remained free from disease for eight months since the surgery.