Abstract
Here I present a case of a 7-year-old girl who presented congenital middle ear cholesteatoma with extensive damage to the ossicles, but without any associate hearing loss. A white mass was identified through the tympanic membrane during a routine school physical examination. Surgical intervention was undertaken, and the decision was made to perform ossicular chain reconstruction using the remaining incus by one-stage tympanoplasty. Here I discuss the surgical strategy, especially the timing of the operation, the type of incision and the ossicular chain reconstruction.
