Abstract
A 69-year-old male presented with complaints of severe headache. MRI revealed that a mass located at the lateral cerebellum invading to the mastoid cavity of the petrous bone. The right external auditory canal (EAC) had no abnormality at the initial visit, but a small hole gradually appeared at the opening of EAC. During surgery, a cholesteatoma mass was removed from the mastoid cavity and the canal wall was reconstructed by a temporal bone fragment. This case could be classified as congenital cholesteatoma because the patient had no history of head injury.
